hrp0092p3-100 | Fat, Metabolism and Obesity | ESPE2019

An Infant with Severe Hypertriglyceridemia: Acute and Long-Term Management in the Paediatric Population

Poon Sarah WY , Tsang Anita MC , Poon Grace WK , Tung Joanna YL

Background: Severe hypertriglyceridemia, defined as triglyceride concentration greater than 11.2 mmol/L, predisposes to acute pancreatitis, a serious complication with mortality rate as high as 6.5% in children (1).Our case highlights the use of insulin infusion to rapidly lower the triglyceride level and the long term management in a young infant with familial chylomicronemia syndrome (FCS) due to lipoprotein lipase deficiency.<stro...